Waltzing with WASP

Trends Cell Biol. 1999 Jan;9(1):15-9. doi: 10.1016/s0962-8924(98)01411-1.

Abstract

Wiskott-Aldrich syndrome (WAS) is an inherited immune deficiency that is marked by eczema, bleeding and recurrent infections. The lymphocytes and platelets of WAS patients display cytoskeletal abnormalities, and their T lymphocytes show a diminished proliferative response to stimulation through the T-cell receptor-CD3 complex (TCR-CD3). The product of the WAS gene, WAS protein (WASP), binds to the small GTPase Cdc42. Small GTPases of the Rho family are crucial for the regulation of the actin-based cytoskeleton. WASP and its relative NWASP might play an important role in regulating the actin cytoskeleton. Since both WASP and NWASP have the potential to bind to multiple proteins, they might serve as a hub to coordinate the redistribution of many cellular signals to the actin cytoskeleton. In this review, the authors discuss the possible role of WASP/NWASP and of the newly described protein WIP, which interacts with WASP and NWASP, in coupling signals from the T-cell receptor to the actin-based cytoskeleton.

Publication types

  • Review

MeSH terms

  • Actins
  • Animals
  • Carrier Proteins / metabolism
  • Cytoskeletal Proteins
  • Cytoskeleton
  • GTP Phosphohydrolases / metabolism
  • GTP-Binding Proteins / metabolism
  • Humans
  • Intracellular Signaling Peptides and Proteins
  • Lymphocytes
  • Proteins / metabolism*
  • Receptor-CD3 Complex, Antigen, T-Cell / metabolism
  • Signal Transduction
  • Wiskott-Aldrich Syndrome / metabolism*
  • Wiskott-Aldrich Syndrome Protein
  • rho GTP-Binding Proteins

Substances

  • Actins
  • Carrier Proteins
  • Cytoskeletal Proteins
  • Intracellular Signaling Peptides and Proteins
  • Proteins
  • Receptor-CD3 Complex, Antigen, T-Cell
  • WAS protein, human
  • WIPF1 protein, human
  • Wiskott-Aldrich Syndrome Protein
  • GTP Phosphohydrolases
  • GTP-Binding Proteins
  • rho GTP-Binding Proteins