Human immunodeficiency virus-associated Hodgkin's disease derives from post-germinal center B cells

Blood. 1999 Apr 1;93(7):2319-26.

Abstract

Human immunodeficiency virus-associated Hodgkin's disease (HIV-HD) displays several peculiarities when compared with HD of the general population. These include overrepresentation of clinically aggressive histologic types and frequent infection of Reed-Sternberg (RS) cells by Epstein-Barr virus (EBV). Recently, we have reported that the histogenesis of HD of the general population may be assessed by monitoring the expression pattern of BCL-6, a transcription factor expressed in germinal center (GC) B cells, and of CD138/syndecan-1 (syn-1), a proteoglycan associated with post-GC, terminal B-cell differentiation. In this study, we have applied these two markers to the study of HIV-HD histogenesis and correlated their expression status to the virologic features of this disease. We have found that RS cells of all histologic categories of HIV-HD consistently display the BCL-6(-)/syn-1(+) phenotype and thus reflect post-GC B cells. Although BCL-6(-)/syn-1(+) RS cells of HIV-HD express CD40, they are not surrounded by CD40 ligand-positive (CD40L+) reactive T lymphocytes, which, in HD of the general population, are thought to regulate the disease phenotype through CD40/CD40L interactions. Conversely, RS cells of virtually all HIV-HD express the EBV-encoded latent membrane protein 1 (LMP1), which, being functionally homologous to CD40, may contribute, at least in part, to the modulation of the HIV-HD phenotype.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • B-Lymphocytes / pathology*
  • Biomarkers, Tumor / analysis
  • CD40 Antigens / analysis
  • CD40 Ligand
  • Cell Communication
  • Cell Differentiation
  • DNA-Binding Proteins / analysis
  • Embryonal Carcinoma Stem Cells
  • Epstein-Barr Virus Infections / complications
  • Epstein-Barr Virus Infections / pathology*
  • Germinal Center / pathology
  • Herpesvirus 4, Human / isolation & purification
  • Hodgkin Disease / etiology
  • Hodgkin Disease / pathology*
  • Hodgkin Disease / virology
  • Humans
  • Lymphoma, AIDS-Related / pathology*
  • Lymphoma, AIDS-Related / virology
  • Membrane Glycoproteins / analysis
  • Neoplasm Proteins / analysis
  • Neoplastic Stem Cells / pathology*
  • Neoplastic Stem Cells / virology
  • Proteoglycans / analysis
  • Proto-Oncogene Proteins / analysis
  • Proto-Oncogene Proteins c-bcl-6
  • Reed-Sternberg Cells / pathology*
  • Reed-Sternberg Cells / virology
  • Syndecan-1
  • Syndecans
  • T-Lymphocytes / chemistry
  • T-Lymphocytes / immunology
  • Transcription Factors / analysis
  • Viral Matrix Proteins / analysis

Substances

  • Biomarkers, Tumor
  • CD40 Antigens
  • DNA-Binding Proteins
  • EBV-associated membrane antigen, Epstein-Barr virus
  • Membrane Glycoproteins
  • Neoplasm Proteins
  • Proteoglycans
  • Proto-Oncogene Proteins
  • Proto-Oncogene Proteins c-bcl-6
  • SDC1 protein, human
  • Syndecan-1
  • Syndecans
  • Transcription Factors
  • Viral Matrix Proteins
  • CD40 Ligand