Experimental partial epileptogenesis

Curr Opin Neurol. 1999 Apr;12(2):203-9. doi: 10.1097/00019052-199904000-00012.

Abstract

Identification of the responsible mutant genes and of the functional consequences of the mutations in experimental preparations have begun to shed light on mechanisms underlying a rare form of partial epilepsy in humans, autosomal dominant nocturnal frontal lobe epilepsy. Likewise, study of the mechanisms of nongenetic models of a common form of human epilepsy, complex partial epilepsy of temporal lobe origin, has established the hippocampal dentate granule cells as a functional barrier to invasion of epileptiform activity into hippocampus in normal brain; this barrier is defective in an epileptic brain. Potential mechanisms by which the 'barrier function' might become flawed, such as mossy fiber sprouting, are discussed.

Publication types

  • Research Support, U.S. Gov't, P.H.S.
  • Review

MeSH terms

  • Animals
  • Disease Models, Animal
  • Epilepsies, Partial / etiology
  • Epilepsies, Partial / physiopathology*
  • Epilepsy, Complex Partial / physiopathology
  • Epilepsy, Frontal Lobe / genetics
  • Epilepsy, Frontal Lobe / physiopathology
  • Epilepsy, Temporal Lobe / physiopathology
  • Hippocampus / physiopathology*
  • Humans
  • Kindling, Neurologic / physiology
  • Mossy Fibers, Hippocampal / physiopathology
  • Nerve Growth Factors / physiology
  • Neural Inhibition / physiology
  • Receptors, Nicotinic / genetics
  • Temporal Lobe / physiopathology*

Substances

  • Nerve Growth Factors
  • Receptors, Nicotinic