Simultaneous occurrence of a vestibular schwannoma and a glomus tympanicum tumor has been reported only once in the international literature. The authors present a second case: a 72-year-old woman having a glomus tympanicum tumor and an ipsilateral lesion confined to the internal auditory canal, radiologically diagnosed as an acoustic neuroma. Due to the patient's age, symptoms, hearing threshold and the small size of both tumors the decision was made not to perform surgery. The patient will be regularly followed-up through computerized tomography and magnetic resonance imaging.