[The young hemophiliac, inhibitors and immune tolerance]

Transfus Clin Biol. 1999 Jun;6(3):191-4. doi: 10.1016/s1246-7820(99)80024-x.
[Article in French]

Abstract

The occurrence of inhibitor in a hemophilic patient is the greatest therapeutic complication in 1999. The inhibitor incidence is higher in hemophilia A (20-30%) than in hemophilia B (3%). At the moment, the best management is immune tolerance induction. This consists in frequent infusion of antihemophilic factor (every day or every other day). The risk of inhibitor development is higher in a young child than in an adult. Consequently, a venous access device is essential for this treatment although not devoid of complications in the young boy. Moreover, the probability of inhibitor disappearance is higher in a child (recent inhibitor) than in an adult ("old" inhibitor).

Publication types

  • English Abstract
  • Review

MeSH terms

  • Adult
  • Child
  • Child, Preschool
  • Desensitization, Immunologic*
  • Factor VIII / immunology*
  • Factor VIII / therapeutic use
  • Factor X / immunology*
  • Factor X / therapeutic use
  • Hemophilia A / immunology*
  • Hemophilia A / therapy
  • Humans
  • Immune Tolerance*
  • Immunization
  • Infant
  • Isoantibodies / immunology*
  • Male
  • Recombinant Fusion Proteins / immunology
  • Recombinant Fusion Proteins / therapeutic use

Substances

  • Isoantibodies
  • Recombinant Fusion Proteins
  • Factor VIII
  • Factor X