Genetics of Alzheimer's disease

Essays Biochem. 1998:33:117-31. doi: 10.1042/bse0330117.

Abstract

Mutations in any one of three genes can cause autosomal dominant, early-onset Alzheimer's disease: these genes are the amyloid precursor protein (APP) gene on chromosome 21, the presenilin-1 (PS-1) gene on chromosome 14 and the presenilin-2 (PS-2) gene on chromosome 1. Pathogenic mutations at all these loci cause mismetabolism of APP such that more of the peptide A beta 42 is produced. This peptide is deposited in the plaques in the brains of Alzheimer's patients. These facts have led to the dominant hypothesis for the disease process: the 'amyloid cascade hypothesis', which proposes that overproduction or failure to clear the peptide A beta 42 is always central to the disease. Genetic variability at the apoliprotein E locus is a major determinant of late onset Alzheimer's disease. The mechanism by which apoliprotein E is involved in the pathogenesis of Alzheimer's disease is not yet known. There are likely to be other genetic factors which impinge on Alzheimer's disease.

Publication types

  • Review

MeSH terms

  • Age of Onset
  • Aged
  • Alzheimer Disease / genetics*
  • Amino Acid Sequence
  • Amyloid beta-Peptides / genetics
  • Amyloid beta-Protein Precursor / genetics
  • Apolipoproteins E / genetics
  • Genes, Dominant
  • Humans
  • Membrane Proteins / chemistry
  • Membrane Proteins / genetics
  • Middle Aged
  • Models, Molecular
  • Molecular Sequence Data
  • Mutation
  • Peptide Fragments / genetics
  • Presenilin-1
  • Presenilin-2
  • Risk Factors

Substances

  • Amyloid beta-Peptides
  • Amyloid beta-Protein Precursor
  • Apolipoproteins E
  • Membrane Proteins
  • PSEN1 protein, human
  • PSEN2 protein, human
  • Peptide Fragments
  • Presenilin-1
  • Presenilin-2
  • amyloid beta-protein (1-42)