Congenital pulmonary venous stenosis presenting as persistent pulmonary hypertension of the newborn

R G Holcomb; R W Tyson; D D Ivy; S H Abman; J P Kinsella

doi:10.1002/(sici)1099-0496(199910)28:4<301::aid-ppul10>3.0.co;2-m

Congenital pulmonary venous stenosis presenting as persistent pulmonary hypertension of the newborn

Pediatr Pulmonol. 1999 Oct;28(4):301-6. doi: 10.1002/(sici)1099-0496(199910)28:4<301::aid-ppul10>3.0.co;2-m.

Authors

R G Holcomb¹, R W Tyson, D D Ivy, S H Abman, J P Kinsella

Affiliation

¹ Section of Neonatology, Pediatric Heart Lung Center, Department of Pediatrics, Children's Hospital, Denver, Colorado 80218, USA.

PMID: 10497380
DOI: 10.1002/(sici)1099-0496(199910)28:4<301::aid-ppul10>3.0.co;2-m

Abstract

Congenital pulmonary venous stenosis (CPVS) has been previously described in older infants and children, typically manifesting as failure to thrive with congestive heart failure and subsequent respiratory deterioration. We report on 2 cases of CPVS which presented during the immediate newborn period as severe persistent pulmonary hypertension of the newborn.

Publication types

Case Reports
Review

MeSH terms

Angiography
Cardiac Catheterization
Constriction, Pathologic / congenital
Constriction, Pathologic / diagnosis
Diagnosis, Differential
Fatal Outcome
Female
Heart Defects, Congenital / diagnosis*
Heart Defects, Congenital / physiopathology
Heart Defects, Congenital / therapy
Humans
Infant, Newborn
Male
Persistent Fetal Circulation Syndrome / diagnosis*
Persistent Fetal Circulation Syndrome / physiopathology
Persistent Fetal Circulation Syndrome / therapy
Pulmonary Veins / abnormalities*
Respiration, Artificial