[Multifocal malignant transformation of extreme fibromatosis with pulmonary involvement]

B Hummel; H J Schumann; B Hofmann; S Baumgärtel; W Rosahl; J Schreiber

doi:10.1055/s-1999-9031

[Multifocal malignant transformation of extreme fibromatosis with pulmonary involvement]

Pneumologie. 1999 Sep;53(9):433-7. doi: 10.1055/s-1999-9031.

[Article in German]

Authors

B Hummel¹, H J Schumann, B Hofmann, S Baumgärtel, W Rosahl, J Schreiber

Affiliation

¹ Klinik für Innere Medizin, Städtisches Klinikum Dessau.

PMID: 10544653
DOI: 10.1055/s-1999-9031

Abstract

We report on the case of a 40-year old patient with extreme neurofibromatosis with severe kyphoskoliosis and deformation of the thorax. The patient died from malignant transformation which occurred multifocally with extensive pulmonary metastases. The well-known thoracic manifestations of neurofibromatosis are reviewed.

Publication types

Case Reports

MeSH terms

Adult
Cell Transformation, Neoplastic
Fatal Outcome
Humans
Kyphosis / complications
Kyphosis / diagnostic imaging
Lung Neoplasms / diagnostic imaging
Lung Neoplasms / pathology
Lung Neoplasms / secondary*
Male
Neurofibromatoses / diagnostic imaging*
Neurofibromatoses / pathology
Scoliosis / complications
Scoliosis / diagnostic imaging
Tomography, X-Ray Computed