Abstract
In 39 patients with myotonic dystrophy, we found a high percentage of infrahissian cardiac conduction abnormalities (51%) and late potentials (46%), whereas spontaneous and inducible ventricular arrhythmias were rare. These results suggest that the prolongation of QRSD and the duration of the low-amplitude signal on the signal-averaged electrocardiogram were related to delayed activation of the His and Purkinje tissue rather than true late potentials.
MeSH terms
-
Adult
-
Atrioventricular Node / physiopathology
-
Bundle of His / physiopathology
-
Cardiac Complexes, Premature / physiopathology
-
Electrocardiography*
-
Electrocardiography, Ambulatory
-
Female
-
Heart Block / diagnosis
-
Heart Block / physiopathology
-
Heart Ventricles / physiopathology*
-
Humans
-
Male
-
Middle Aged
-
Myotonic Dystrophy / diagnosis
-
Myotonic Dystrophy / physiopathology*
-
Purkinje Fibers / physiopathology
-
Risk Factors
-
Signal Processing, Computer-Assisted*