Narrowing of the region of allelic loss in 21q11-21 in squamous non-small cell lung carcinoma and cloning of a novel ubiquitin-specific protease gene from the deleted segment

Genes Chromosomes Cancer. 2000 Feb;27(2):153-61.

Abstract

We examined 42 fresh non-small cell lung carcinomas for allelic loss using 4 microsatellite markers located in a 4.5 Mb region in 21q11-21, a gene-poor interval recently found by others to be homozygously deleted and exhibiting frequent allelic loss in lung cancer. We found allelic loss across the entire segment in 13/34 informative squamous carcinomas, with 2 cases showing loss in only part of the region. Analysis by fluorescence in situ hybridization of P1-derived artificial chromosomes from the region directly on paraffin sections of the tumor is in concordance with the loss of heterozygosity (LOH) results, and tentatively excludes a 2 Mb segment bearing 2 of the only 3 known genes in the area. Exon trapping in the remaining segment of loss led to identification and cloning of a novel gene spanning 150 kb within the deletion. The full-length gene encodes a protein of 1,055 amino acids with homology to ubiquitin-specific proteases across the eukaryotic evolutionary spectrum. The expressed protein acts as a de-ubiquitinating enzyme as proved by the ability to cleave ubiquitin from a model fusion protein. We found no mutations in the sequence of the functional domains of this gene in any of the LOH-exhibiting tumor DNA samples. It is, however, interesting that genes of the same superfamily have been reported on 3p21, a locus showing the most frequent allelic instability and deletions in lung cancer. Genes Chromosomes Cancer 27:153-161, 2000.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Amino Acid Sequence
  • Carcinoma, Non-Small-Cell Lung / genetics*
  • Carcinoma, Squamous Cell / genetics*
  • Chromosomes, Human, Pair 21 / genetics*
  • Cloning, Molecular
  • DNA / chemistry
  • DNA / genetics
  • Endopeptidases / genetics*
  • Endopeptidases / metabolism
  • Exons
  • Genetic Vectors
  • Humans
  • In Situ Hybridization, Fluorescence
  • Loss of Heterozygosity
  • Lung Neoplasms / genetics*
  • Microsatellite Repeats
  • Molecular Sequence Data
  • Recombinant Fusion Proteins / genetics
  • Recombinant Fusion Proteins / metabolism
  • Sequence Analysis, DNA
  • Sequence Deletion
  • Sequence Homology, Amino Acid
  • Ubiquitin-Specific Proteases
  • Ubiquitins / genetics
  • Ubiquitins / metabolism

Substances

  • Recombinant Fusion Proteins
  • Ubiquitins
  • DNA
  • Endopeptidases
  • Ubiquitin-Specific Proteases

Associated data

  • GENBANK/AF134213