Mutation detection by TaqMan-allele specific amplification: application to molecular diagnosis of glycogen storage disease type Ia and medium-chain acyl-CoA dehydrogenase deficiency

Hum Mutat. 2000;15(2):189-96. doi: 10.1002/(SICI)1098-1004(200002)15:2<189::AID-HUMU8>3.0.CO;2-H.

Abstract

We have devised an allele-specific amplification method with a TaqMan fluorogenic probe (TaqMan-ASA) for the detection of point mutations. Pairwise PCR amplification using two sets of allele-specific primers in the presence of a TaqMan probe was monitored in real time with a fluorescence detector. Difference in amplification efficiency between the two PCR reactions was determined by "threshold" cycles to differentiate mutant and normal alleles without post-PCR processing. The method measured the efficiency of amplification rather than the presence or absence of end-point PCR products, therefore allowing greater flexibility in designing allele-specific primers and an ample technical margin for allelic discrimination. We applied the TaqMan-ASA method to detect a prevalent 727G>T mutation in Japanese patients with glycogen storage disease type Ia and a common 985A>G mutation in Caucasian patients with medium-chain acyl-CoA dehydrogenase deficiency. The method can be automated and may be applicable to the DNA diagnosis of various genetic diseases.

MeSH terms

  • Acyl-CoA Dehydrogenase
  • Acyl-CoA Dehydrogenases / deficiency
  • Acyl-CoA Dehydrogenases / genetics*
  • Alleles*
  • Base Pair Mismatch / genetics
  • DNA Mutational Analysis / methods*
  • DNA Primers
  • DNA Probes
  • Dose-Response Relationship, Drug
  • Fluorescent Dyes
  • Genetic Testing / methods
  • Genotype
  • Glycogen Storage Disease Type I / diagnosis
  • Glycogen Storage Disease Type I / genetics*
  • Humans
  • Japan
  • Point Mutation / genetics*
  • Polymerase Chain Reaction / methods
  • Sensitivity and Specificity
  • Taq Polymerase / metabolism*
  • Templates, Genetic
  • Time Factors
  • White People / genetics

Substances

  • DNA Primers
  • DNA Probes
  • Fluorescent Dyes
  • Acyl-CoA Dehydrogenases
  • Acyl-CoA Dehydrogenase
  • Taq Polymerase