Identification of three rare beta-thalassemia mutations in the Pakistani population

Hemoglobin. 2000 Feb;24(1):15-22. doi: 10.3109/03630260009002269.

Abstract

Three rare beta-thalassemia mutations, not reported previously in Asian Indians or the Pakistani population, were identified by single strand conformation polymorphism analysis followed by direct sequencing. Two mutations, IVS-II-848 (C-->A) and initiation codon (ATG-->ACG), were found in the homozygous condition in patients belonging to Balochi and Sindhi ethnic groups of Pakistan, together with heterozygous and homozygous alpha(-3.7) deletions, respectively. A frameshift mutation at codon 44 (-C) was identified in a patient belonging to the Gujrati ethnic group together with IVS-I-1 (G-->T) and a normal complement of four a-globin genes. Haplotype analysis was performed to identify the chromosomal background associated with these mutations, and for tracing the origin and spread of these mutations.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Amino Acid Substitution
  • DNA Mutational Analysis
  • Ethnicity / genetics
  • Family Health
  • Female
  • Frameshift Mutation
  • Genetic Testing
  • Haplotypes
  • Hemoglobins, Abnormal / genetics
  • Heterozygote
  • Homozygote
  • Humans
  • Infant
  • Male
  • Pakistan / epidemiology
  • Pakistan / ethnology
  • Point Mutation
  • Polymorphism, Single-Stranded Conformational
  • beta-Thalassemia / epidemiology*
  • beta-Thalassemia / genetics*

Substances

  • Hemoglobins, Abnormal