[Contribution of medical imaging to visceral manifestations of sickle cell anemia in the child]

Dakar Med. 1999;44(1):36-9.
[Article in French]

Abstract

Sickle cell anemia is one of the qualitative hemoglobinopathies which are the most widespread in the world. In a retrospective study on 11 drepanocytary patients (10 SS and 1 SC) observed at the BORDEAUX children's hospital. 3 Processus were identified: Hemolysis: 3 hepatomegaly, 3 splenomegaly, 1 hematochromatosis and 4 pigmentary lithiasis; Thrombosis: 1 infarctus case of spleen, kidney, lung, 1 papillary necrosis and 1 brain vascular ischemic appearance;

Infection: 1 spleen abscess and 1 pneumopathy. In 15% of instances, visceral appearances are allowed to discoverer sickle cell anemia. Hemolysis type appearances were currently observed (63.6%) like pigmentary lithiasis and hepatomegaly. The authors analyze the major radiological appearances of this hemoglobinopathy and recall the interest in knowing this disease even in low endemicity countries.

MeSH terms

  • Adolescent
  • Anemia, Sickle Cell / complications
  • Anemia, Sickle Cell / diagnostic imaging*
  • Cardiomegaly / diagnosis
  • Cardiomegaly / etiology
  • Child
  • Hemolysis
  • Hepatomegaly / diagnosis
  • Hepatomegaly / etiology
  • Humans
  • Infarction / diagnosis
  • Infarction / etiology
  • Infections / diagnosis
  • Infections / etiology
  • Radiography
  • Retrospective Studies
  • Splenomegaly / diagnosis
  • Splenomegaly / etiology
  • Thrombosis / diagnosis
  • Thrombosis / etiology