Phytanic acid alpha-oxidation in man: identification of 2-hydroxyphytanoyl-CoA lyase, a peroxisomal enzyme with normal activity in Zellweger syndrome

J Inherit Metab Dis. 2000 Jun;23(4):421-4. doi: 10.1023/a:1005672406773.
No abstract available

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Carbon-Carbon Lyases / metabolism*
  • Humans
  • Liver / enzymology
  • Male
  • Oxidation-Reduction
  • Peroxisomes / enzymology
  • Phytanic Acid / metabolism*
  • Zellweger Syndrome / enzymology*

Substances

  • Phytanic Acid
  • Carbon-Carbon Lyases
  • 2-hydroxyphytanoyl-coenzyme A lyase