Increased risk of lymphoproliferative disorders in relatives of patients with B-cell chronic lymphocytic leukemia: relevance of the degree of familial linkage

Eur J Haematol. 2000 Aug;65(2):114-7. doi: 10.1034/j.1600-0609.2000.90183.x.

Abstract

We assessed the familial aggregation of chronic lymphoproliferative diseases (CLD) in 3962 relatives of 169 patients with B-cell chronic lymphocytic leukemia (B-CLL). Data collection included a self-administered questionnaire. The "relative risk" considered the connection between a higher incidence of CLD and the degree of familial linkage with the probands. The model of logistic regression was statistically significant (p < 0.001), with the probability of CLD increasing in proportion to the relationship coefficient between parents, siblings and children [(relationship coefficient 0.5; probability of CLD 1.85 (C.I. 95%, range 1.1-3%)]. CLD, particularly B-CLL, were observed in first-degree relatives of the patients with B-CLL more often than in other relatives.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, Non-P.H.S.

MeSH terms

  • Adult
  • Aged
  • Aged, 80 and over
  • Chronic Disease
  • Family Health
  • Female
  • Genetic Linkage / genetics*
  • Genetic Predisposition to Disease / genetics
  • Hematologic Neoplasms / genetics
  • Humans
  • Leukemia, Lymphocytic, Chronic, B-Cell / genetics*
  • Lymphoproliferative Disorders / genetics*
  • Male
  • Middle Aged
  • Surveys and Questionnaires