Parkin is metabolized by the ubiquitin/proteosome system

Neuroreport. 2000 Aug 21;11(12):2635-8. doi: 10.1097/00001756-200008210-00006.

Abstract

Mutations in the parkin gene cause autosomal recessive juvenile parkinsonism. Immunostaining of substantia nigra sections from sporadic Parkinson's disease (PD) cases shows that Parkin accumulates in axonal spheroids and in some Lewy bodies. Because ubiquitin is a major component of Lewy bodies and axonal spheroids, we investigated whether Parkin is metabolized via the ubiquitin/proteosomal pathway. Treatment of BE-M17 neuroblastoma cells with the proteosomal inhibitor, MG132, produced a band corresponding to di-ubiquitinated Parkin that was apparent by immunoblot using two different anti-Parkin antibodies. This higher mol. wt band also co-immunoprecipitated with Parkin. These data suggest that Parkin plays a role in the pathophysiology of sporadic PD, and that Parkin is a substrate for ubiquitination that is degraded by the proteosomal complex.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Aged
  • Antibodies / pharmacology
  • Cysteine Endopeptidases / metabolism*
  • Humans
  • Immunoblotting
  • Immunohistochemistry
  • Leupeptins / pharmacology
  • Ligases / immunology
  • Ligases / metabolism*
  • Middle Aged
  • Multienzyme Complexes / antagonists & inhibitors
  • Multienzyme Complexes / metabolism*
  • Parkinson Disease / metabolism
  • Precipitin Tests
  • Proteasome Endopeptidase Complex
  • Reference Values
  • Substantia Nigra / metabolism*
  • Substrate Specificity
  • Tumor Cells, Cultured
  • Ubiquitin-Protein Ligases
  • Ubiquitins / metabolism*

Substances

  • Antibodies
  • Leupeptins
  • Multienzyme Complexes
  • Ubiquitins
  • Ubiquitin-Protein Ligases
  • Cysteine Endopeptidases
  • Proteasome Endopeptidase Complex
  • Ligases
  • benzyloxycarbonylleucyl-leucyl-leucine aldehyde