Abstract
Life-threatening haemolysis in children with autoimmune haemolytic anaemia (AIHA) occurs rarely. Many cases of severe autoimmune disease are currently treated with immunosuppressive high-dose chemotherapy and autograft. We report here a case of a child with severe AIHA who did not respond to conventional treatments, but was cured with an autologous peripheral blood CD34(+) cell transplantation. After d 16 post autograft, no further red cell transfusions were required. At 20 months post autograft, haematological complete remission persists.
MeSH terms
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Anemia, Hemolytic, Autoimmune / therapy*
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Antigens, CD34*
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Antineoplastic Combined Chemotherapy Protocols / therapeutic use
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Carmustine / therapeutic use
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Child
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Cyclophosphamide / therapeutic use
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Cytarabine / therapeutic use
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Hematopoietic Stem Cell Mobilization
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Hematopoietic Stem Cell Transplantation*
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Humans
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Immunoglobulins, Intravenous
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Immunosuppressive Agents / therapeutic use
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Male
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Melphalan / therapeutic use
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Methylprednisolone / therapeutic use
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Plasmapheresis
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Podophyllotoxin / therapeutic use
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Prednisolone / therapeutic use
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Splenectomy
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Stem Cells / immunology*
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Transplantation, Autologous
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Treatment Outcome
Substances
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Antigens, CD34
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Immunoglobulins, Intravenous
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Immunosuppressive Agents
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Cytarabine
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Cyclophosphamide
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Prednisolone
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Podophyllotoxin
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Melphalan
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Carmustine
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Methylprednisolone