Alveolar soft-part sarcoma of the cheek: report of a case with a review of the literature

Int J Oral Maxillofac Surg. 2000 Oct;29(5):366-9.

Abstract

An alveolar soft-part sarcoma (ASPS) occurring in the cheek is described, with a review of the literature. The subject was a 25-year-old woman who presented with a large swelling in the left cheek. The lesion, initially diagnosed as a benign tumor on radiographic and computed tomographic examinations, was surgically excised. Histopathological examination of the mass revealed a nest-like or organoid cellular arrangement as confirmed by three-dimensional computer graphic reconstruction. The cytoplasm of the large polygonal tumor cells contained abundant diastase-resistant, PAS-positive inclusions, ultrastructurally confirmed to be crystalloid materials. The tumor cells were immunoreactive for anti-myoglobin, sarcomeric actin, and neuron-specific enolase antibodies, suggesting a myogenic origin.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Adult
  • Cheek
  • Female
  • Humans
  • Immunohistochemistry
  • Mouth Neoplasms / diagnosis*
  • Mouth Neoplasms / pathology
  • Mouth Neoplasms / surgery
  • Sarcoma, Alveolar Soft Part / diagnosis*
  • Sarcoma, Alveolar Soft Part / pathology
  • Sarcoma, Alveolar Soft Part / surgery