[From gene to disease; from p16 to melanoma]

Ned Tijdschr Geneeskd. 2000 Oct 28;144(44):2100-2.
[Article in Dutch]

Abstract

Approximately 10% of human cutaneous melanoma cases occur in families with the familial atypical multiple mole melanoma (FAMMM) syndrome, which is characterised by the familial occurrence of melanomas and atypical precursor naevi. A melanoma-associated gene has been mapped to 9p2l, encoding for the tumour suppressor gene CDKN2A. Worldwide, germline mutations in melanoma kindreds implicate this cell cycle regulator (p16) as a susceptibility gene for malignant melanoma. Most FAMMM families registered at the Leiden Pigmented Lesions Clinic share the same CDKN2A inactivating deletion (P16-Leiden). Presymptomatic DNA diagnosis will now be available for P16-Leiden positive FAMMM family members at the Leiden University Medical Centre.

Publication types

  • English Abstract
  • Review

MeSH terms

  • Cell Division
  • Cyclin-Dependent Kinase Inhibitor p16 / genetics*
  • Dysplastic Nevus Syndrome / genetics*
  • Genes, p16 / genetics*
  • Genetic Predisposition to Disease
  • Genetic Testing
  • Humans
  • Melanoma / genetics*
  • Mutation*
  • Netherlands
  • Skin Neoplasms / genetics*

Substances

  • Cyclin-Dependent Kinase Inhibitor p16