Roles of phosphate and an enoyl radical in ferritin iron mobilization by 5-aminolevulinic acid

Free Radic Biol Med. 2000 Dec 15;29(12):1272-9. doi: 10.1016/s0891-5849(00)00437-8.

Abstract

5-Aminolevulinic acid (ALA), a heme precursor that accumulates in acute intermittent porphyria (AIP) and lead poisoning, undergoes enolization and subsequent iron-catalyzed oxidation at neutral pH. Iron is released from horse spleen ferritin (HoSF) by both ALA-generated O(2)(.-) and enoyl radical (ALA(z.rad)), which amplifies the chain of ALA oxidation (autocatalysis). Iron chelators such as EDTA, ATP, but not citrate, and phosphate accelerate this process and ALA-promoted iron release from HoSF is faster in horse spleen isoferritins containing larger amounts of phosphate in the core. ALA (+0.377 V versus standard hydrogen electrode) is less effective in releasing iron from ferritin than are thioglycollic acid, 6-hydroxydopamine, and N,N,N', N'-tetramethyl-p-phenylenediamine. During electrochemical one electron oxidation of ALA in a nitrogen atmosphere, spin trapping experiments with 3,5-dibromo-4-nitrosobenzenesulfonic acid demonstrated the formation of a spin adduct characterized by a six line signal, indicating a secondary carbon-centered radical and attributed to a resonant ALA&z.rad; radical. Iron is also released in such anaerobic electrochemical oxidations of ALA in the presence of ferritin, suggesting that, in addition to O(2)(*-), ALA&z.rad; can promote iron mobilization from ferritin. Hence, ALA&z.rad; may amplify the metal-catalyzed oxidation of ALA, damaging ALA-accumulating cells and possibly contributing to the symptoms of porphyria.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adenosine Triphosphate / chemistry
  • Aminolevulinic Acid / chemistry*
  • Ferritins / chemistry*
  • Free Radicals
  • Iron / chemistry*
  • Kinetics
  • Oxidation-Reduction
  • Oxidopamine / chemistry
  • Phosphates / chemistry*
  • Potentiometry
  • Superoxides / chemistry*
  • Tetramethylphenylenediamine / chemistry
  • Thioglycolates / chemistry

Substances

  • Free Radicals
  • Phosphates
  • Thioglycolates
  • Superoxides
  • Aminolevulinic Acid
  • Oxidopamine
  • Adenosine Triphosphate
  • Ferritins
  • Iron
  • Tetramethylphenylenediamine