Molecular cytogenetic definition of 17q translocation breakpoints in neuroblastoma

Med Pediatr Oncol. 2001 Jan;36(1):20-3. doi: 10.1002/1096-911X(20010101)36:1<20::AID-MPO1006>3.0.CO;2-E.

Abstract

Background: Unbalanced translocations resulting in the gain of material from 17q are the most common chromosomal changes in neuroblastoma and are associated with poor patient survival, and are established indicators of bad prognosis.

Procedure: We have used 13 fluorescent in situ hybridisation probes to map 17q translocation breakpoints in ten neuroblastoma cell lines and 21 primary tumours.

Results: At least seven different breakpoints have been identified, all localised within the proximal half of 17q (53-68 cM, 17cen-17q22).

Conclusion: These results suggest that the dosage of a gene, or genes, in 17q22-qter is responsible for the clinical effects of 17q gain, rather than the disruption of a specific gene.

Publication types

  • Comparative Study
  • Multicenter Study
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Chromosome Breakage*
  • Chromosome Mapping
  • Chromosomes, Human, Pair 17 / genetics
  • Chromosomes, Human, Pair 17 / ultrastructure*
  • DNA Probes
  • Gene Dosage
  • Humans
  • In Situ Hybridization, Fluorescence
  • Neuroblastoma / genetics*
  • Neuroblastoma / mortality
  • Neuroblastoma / ultrastructure
  • Prognosis
  • Translocation, Genetic*
  • Tumor Cells, Cultured / ultrastructure

Substances

  • DNA Probes