Haemoglobin Titusville: alpha94 Asp replaced by Asn. A new haemoglobin with a lowered affinity for oxygen

Biochim Biophys Acta. 1975 Aug 19;400(2):365-73.

Abstract

A new haemoglobin variant with a decreased oxygen affinity is described, in which the substitution, alpha 94 (G1) Asp replaced by Asn, affects the alpha1beta2 contact alpha1G1-beta2G4. The relevance of this variant to our understanding of the importance of the hydrogen bond between alpha1G1 and beta2G4 in Perutz's model of oxyhaemoglobin A is discussed.

MeSH terms

  • Asparagine / analysis
  • Aspartic Acid / analysis
  • Binding Sites
  • Child, Preschool
  • Female
  • Hemoglobins
  • Hemoglobins, Abnormal*
  • Humans
  • Kansas
  • Kinetics
  • Macromolecular Substances
  • Oxygen / blood*
  • Peptide Fragments / analysis
  • Phytic Acid / blood
  • Protein Binding
  • Texas

Substances

  • Hemoglobins
  • Hemoglobins, Abnormal
  • Macromolecular Substances
  • Peptide Fragments
  • Aspartic Acid
  • Asparagine
  • Phytic Acid
  • Oxygen