Loss of the Suv39h histone methyltransferases impairs mammalian heterochromatin and genome stability

Cell. 2001 Nov 2;107(3):323-37. doi: 10.1016/s0092-8674(01)00542-6.

Abstract

Histone H3 lysine 9 methylation has been proposed to provide a major "switch" for the functional organization of chromosomal subdomains. Here, we show that the murine Suv39h histone methyltransferases (HMTases) govern H3-K9 methylation at pericentric heterochromatin and induce a specialized histone methylation pattern that differs from the broad H3-K9 methylation present at other chromosomal regions. Suv39h-deficient mice display severely impaired viability and chromosomal instabilities that are associated with an increased tumor risk and perturbed chromosome interactions during male meiosis. These in vivo data assign a crucial role for pericentric H3-K9 methylation in protecting genome stability, and define the Suv39h HMTases as important epigenetic regulators for mammalian development.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Aneuploidy
  • Animals
  • Chromosome Segregation / physiology*
  • Fibroblasts / cytology
  • Gene Targeting / methods
  • Genome
  • Germ Cells
  • Heterochromatin / physiology*
  • Histone Methyltransferases
  • Histone-Lysine N-Methyltransferase / genetics
  • Histone-Lysine N-Methyltransferase / physiology*
  • Histones / metabolism
  • Hypogonadism
  • Lymphoma, B-Cell
  • Male
  • Mammals
  • Meiosis
  • Methylation
  • Methyltransferases / genetics
  • Methyltransferases / physiology*
  • Mice
  • Mice, Knockout
  • Mice, Mutant Strains
  • Mutagenesis
  • Protein Methyltransferases
  • Repressor Proteins / genetics
  • Repressor Proteins / physiology*
  • Sex Chromosome Aberrations*
  • Spermatocytes
  • Spermatogenesis / genetics
  • Spermatogenesis / physiology

Substances

  • Heterochromatin
  • Histones
  • Repressor Proteins
  • Suv39h1 protein, mouse
  • Histone Methyltransferases
  • Methyltransferases
  • Protein Methyltransferases
  • Histone-Lysine N-Methyltransferase