Objective: To call attention to the rare involvement of pulmonary artery by sarcoma.
Methods: To summarize the clinical, radiological and pathologic features of a case of pulmonary artery sarcoma.
Results: Pulmonary artery sarcoma has similar clinical manifestations as other pulmonary artery obstructive diseases (including pulmonary thromboembolism). The diagnosis should be considered in the patient with clinical presentations suggested pulmonary embolism. The radiological findings included unilateral hilar enlargement, contiguously soft tissue-filled pulmonary artery and pulmonary nodules and clinically deterioration was found after anticoagulant therapy.
Conclusion: Pulmonary artery sarcoma is usually misdiagnosed as other pulmonary artery obstructive diseases. More attention should be paid to it.