Fine specificity of autoantibodies to soluble liver antigen and liver/pancreas

Hepatology. 2002 Feb;35(2):403-8. doi: 10.1053/jhep.2002.30699.

Abstract

Autoantibodies to soluble liver antigen and liver pancreas (SLA/LP) have been described as specific markers for Autoimmune Hepatitis (AIH), occurring in about 20% of patients with AIH. The high degree of specificity for SLA/LP in autoimmune liver disease suggests a possible role in its pathogenesis. This study aims to map the exact epitope(s) recognized by SLA/LP autoantibodies and to assess the role of molecular mimicry between microbial antigens and self-epitopes. Using SLA/LP-reactive sera of 18 individual AIH patients and a pool of 15 patient sera, we found the dominant immune reactivity directed to peptide p395-414 and a less prominent immune response to 2 other epitopes adjacent to the dominant epitope. Immunodominance of peptide p395-414 was confirmed by absorption experiments. The SLA/LP autoantibodies of all tested AIH patients were mainly of the IgG1 type, suggesting that SLA/LP autoantibodies may arise by a common and specific underlying immune stimulus. Based on sequence homologies of the SLA/LP antigenic region with viral proteins, it was hypothesized that molecular mimicry may drive autoimmunity to SLA/LP. However, the homologous virus-derived peptides were not recognized by SLA/LP autoantibodies. Similarly, the only known procaryotic homologue, MJ0610 of Methanococcus jannaschii, was only weakly recognized by SLA/LP-positive sera. Thus, no evidence could be found for molecular mimicry being the causative mechanism for the development of SLA/LP autoantibodies. In conclusion, the exquisite epitope specificity and IgG subtype are evidence for the maturity of the SLA/LP autoantibody response; a specific autoantigen-driven process underlying the immunopathogenesis is likely.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Antibody Specificity
  • Antigens, Bacterial / genetics
  • Antigens, Bacterial / immunology
  • Antigens, Viral / immunology
  • Autoantibodies / immunology*
  • Autoantigens / chemistry
  • Autoantigens / immunology*
  • Cross Reactions
  • Epitopes
  • Hepatitis, Autoimmune / immunology*
  • Humans
  • Immunoglobulin G / immunology
  • Immunoglobulin Isotypes / immunology
  • Molecular Mimicry
  • Peptide Fragments / immunology

Substances

  • Antigens, Bacterial
  • Antigens, Viral
  • Autoantibodies
  • Autoantigens
  • Epitopes
  • Immunoglobulin G
  • Immunoglobulin Isotypes
  • Peptide Fragments
  • liver antigen LA-1