A p38 MAPK inhibitor, FR-167653, ameliorates murine bleomycin-induced pulmonary fibrosis

Am J Physiol Lung Cell Mol Physiol. 2002 Jul;283(1):L103-12. doi: 10.1152/ajplung.00187.2001.

Abstract

To elucidate the pathophysiology of pulmonary fibrosis, we investigated the involvement of p38 mitogen-activated protein kinase (MAPK), which is one of the major signal transduction pathways of proinflammatory cytokines, in a murine model of bleomycin-induced lung fibrosis. p38 MAPK and its substrate, activating transcription factor (ATF)-2, in bronchoalveolar lavage fluid cells were phosphorylated by intratracheal exposure of bleomycin, and the phosphorylation of ATF-2 was inhibited by subcutaneous administration of a specific inhibitor of p38 MAPK, FR-167653. FR-167653 also inhibited augmented expression of tumor necrosis factor -alpha, connective tissue growth factor, and apoptosis of lung cells induced by bleomycin administration. Moreover, daily subcutaneous administration of FR-167653 (from 1 day before to 14 days after bleomycin administration) ameliorated pulmonary fibrosis and pulmonary cachexia induced by bleomycin. These findings demonstrated that p38 MAPK is involved in bleomycin-induced pulmonary fibrosis, and its inhibitor, FR-167653, may be a feasible therapeutic agent.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Activating Transcription Factor 2
  • Animals
  • Antibiotics, Antineoplastic
  • Bleomycin
  • Bronchoalveolar Lavage Fluid / cytology
  • Connective Tissue Growth Factor
  • Cyclic AMP Response Element-Binding Protein / metabolism
  • Disease Models, Animal
  • Gene Expression / drug effects
  • Growth Inhibitors / pharmacology*
  • Growth Substances / genetics
  • Hydroxyproline / analysis
  • Immediate-Early Proteins / genetics
  • In Situ Nick-End Labeling
  • Injections, Intravenous
  • Intercellular Signaling Peptides and Proteins*
  • Lung / chemistry
  • Lung / enzymology
  • Lung / pathology
  • Male
  • Mice
  • Mice, Inbred ICR
  • Mitogen-Activated Protein Kinases / antagonists & inhibitors*
  • Mitogen-Activated Protein Kinases / metabolism
  • Phosphorylation
  • Pulmonary Fibrosis / drug therapy*
  • Pulmonary Fibrosis / metabolism*
  • Pulmonary Fibrosis / pathology
  • Pyrazoles / pharmacology*
  • Pyridines / pharmacology*
  • RNA, Messenger / analysis
  • Transcription Factors / metabolism
  • Transforming Growth Factor beta / genetics
  • Tumor Necrosis Factor-alpha / genetics
  • Tumor Necrosis Factor-alpha / metabolism
  • Weight Gain / drug effects
  • p38 Mitogen-Activated Protein Kinases

Substances

  • Activating Transcription Factor 2
  • Antibiotics, Antineoplastic
  • Atf2 protein, mouse
  • CCN2 protein, mouse
  • Cyclic AMP Response Element-Binding Protein
  • FR 167653
  • Growth Inhibitors
  • Growth Substances
  • Immediate-Early Proteins
  • Intercellular Signaling Peptides and Proteins
  • Pyrazoles
  • Pyridines
  • RNA, Messenger
  • Transcription Factors
  • Transforming Growth Factor beta
  • Tumor Necrosis Factor-alpha
  • Bleomycin
  • Connective Tissue Growth Factor
  • Mitogen-Activated Protein Kinases
  • p38 Mitogen-Activated Protein Kinases
  • Hydroxyproline