[Castleman's disease. Discussion related to case report]

Rev Med Chir Soc Med Nat Iasi. 2000 Jul-Sep;104(3):133-41.
[Article in Romanian]

Abstract

Castleman's disease, also called angiofollicular hyperplasia was first described as a distinct entity by Castleman et al in 1956. Now there are described two forms, a localised and a multicentric one. All forms of disease share the same histopathological features with a highly characteristic angiofollicular lymphoid hyperplasia which is either hyalinovascular or plasmocytic. The clinical and biological signs are varied and heterogeneous. The disorder is of unknown origin, but interleukin 6 plays a central part in this disease. Despite the benignity of this "prelymphoma state", an aggressive course with poor prognosis occur usually in the multicentric form. We report a case of Castleman's disease, multicentric variant. This case provides the opportunity for discussing many aspects of this atypical lymphoproliferative disorder.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Aged
  • Anti-Inflammatory Agents / therapeutic use
  • Castleman Disease / diagnosis*
  • Castleman Disease / drug therapy
  • Castleman Disease / pathology
  • Castleman Disease / physiopathology
  • Diagnosis, Differential
  • Humans
  • Interleukin-6 / metabolism
  • Male
  • Prognosis
  • Severity of Illness Index
  • Steroids

Substances

  • Anti-Inflammatory Agents
  • Interleukin-6
  • Steroids