Delayed apoptotic cell clearance and lupus-like autoimmunity in mice lacking the c-mer membrane tyrosine kinase

J Exp Med. 2002 Jul 1;196(1):135-40. doi: 10.1084/jem.20012094.

Abstract

Mice lacking the membrane tyrosine kinase c-mer have been shown to have altered macro-phage cytokine production and defective phagocytosis of apoptotic cells despite normal phagocytosis of other particles. We show here that c-mer-deficient mice have impaired clearance of infused apoptotic cells and that they develop progressive lupus-like autoimmunity, with antibodies to chromatin, DNA, and IgG. The autoimmunity appears to be driven by endogenous antigens, with little polyclonal B cell activation. These mice should be an excellent model for studying the role of apoptotic debris as an immunogenic stimulus for systemic autoimmunity.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, Non-P.H.S.
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Animals
  • Apoptosis / immunology*
  • Autoantibodies / blood
  • Autoimmunity / immunology*
  • B-Lymphocytes / immunology
  • Cardiolipins / immunology
  • Chromatin / immunology
  • DNA / immunology
  • Disease Models, Animal
  • Female
  • Fluorescent Dyes
  • Glomerular Mesangium / pathology
  • Immunoglobulin G / immunology
  • Lupus Erythematosus, Systemic / complications
  • Lupus Erythematosus, Systemic / immunology*
  • Male
  • Mice
  • Mice, Inbred C57BL
  • Mice, Mutant Strains
  • Phagocytosis / immunology
  • Protein-Tyrosine Kinases / deficiency*
  • Protein-Tyrosine Kinases / genetics
  • Proteinuria / complications
  • Proteinuria / pathology
  • Proto-Oncogene Proteins / deficiency*
  • Proto-Oncogene Proteins / genetics
  • Receptor Protein-Tyrosine Kinases*
  • Rheumatoid Factor / blood
  • Rhodamines
  • c-Mer Tyrosine Kinase

Substances

  • 5-carboxytetramethylrhodamine succinimidyl ester
  • Autoantibodies
  • Cardiolipins
  • Chromatin
  • Fluorescent Dyes
  • Immunoglobulin G
  • Proto-Oncogene Proteins
  • Rhodamines
  • DNA
  • Rheumatoid Factor
  • Mertk protein, mouse
  • Protein-Tyrosine Kinases
  • Receptor Protein-Tyrosine Kinases
  • c-Mer Tyrosine Kinase