Abstract
Expression profile analysis demonstrated that the expression of membrane-associated transporter protein (MATP) varied similarly to the melanogenic enzymes dopachrome tautomerase (DCT) and tyrosinase related protein 1 (TYRP1) (Proc. Natl Acad. Sci. USA (2002) in press). Mutations in MATP result in pigmentation alterations in mice (underwhite, uw), in medaka (b-locus), and in man (Oculocutaneous Albinism Type 4, OCA4) (Nat. Genet. 28 (2001) 381; Am. J. Hum. Genet. 69 (2001) 981). Consistent with MATP acting in a pigment cell autonomous manner, in situ hybridization analysis demonstrated expression of murine Matp in the presumptive retinal pigmented epithelium starting at E9.5, and in neural crest-derived melanoblasts starting at E10.5. Matp expression is reduced in embryos mutated for microphthalmia-associated transcription factor (Mitf) (Cell 74 (1993) 395; J. Biol. Chem. 268 (1993) 20687), suggesting Mitf regulates Matp expression.
MeSH terms
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Albinism, Oculocutaneous / embryology*
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Albinism, Oculocutaneous / genetics*
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Albinism, Oculocutaneous / pathology
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Animals
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Antigens, Neoplasm
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DNA-Binding Proteins / genetics
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Gene Expression Regulation, Developmental
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Genetic Markers
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Humans
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In Situ Hybridization
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Intramolecular Oxidoreductases / genetics
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Melanocytes / metabolism
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Melanocytes / pathology
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Membrane Glycoproteins*
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Membrane Proteins*
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Membrane Transport Proteins
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Mice
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Microphthalmia-Associated Transcription Factor
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Mutation
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Oxidoreductases*
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Pigment Epithelium of Eye / embryology
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Pigment Epithelium of Eye / metabolism
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Pigment Epithelium of Eye / pathology
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Proteins / genetics*
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Stem Cells / metabolism
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Stem Cells / pathology
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Symporters
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Transcription Factors / genetics
Substances
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Antigens, Neoplasm
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DNA-Binding Proteins
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Genetic Markers
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MITF protein, human
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Matp protein, mouse
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Membrane Glycoproteins
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Membrane Proteins
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Membrane Transport Proteins
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Microphthalmia-Associated Transcription Factor
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Mitf protein, mouse
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Proteins
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SLC45A2 protein, human
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Symporters
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Transcription Factors
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Oxidoreductases
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TYRP1 protein, human
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Tyrp1 protein, mouse
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tyrosinase-related protein-1
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Intramolecular Oxidoreductases
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dopachrome isomerase