Dopamine transmission in DYT1 dystonia: a biochemical and autoradiographical study

Neurology. 2002 Aug 13;59(3):445-8. doi: 10.1212/wnl.59.3.445.

Abstract

Indices of dopamine transmission were measured in the postmortem striatum of DYT1 dystonia brains. A significant increase in the striatal 3,4-dihydroxyphenylacetic acid/dopamine ratio was found. Quantitative autoradiography revealed no differences in the density of dopamine transporter or vesicular monoamine transporter-2 binding; however, there was a trend toward a reduction in D(1) receptor and D(2) receptor binding. One brain with DYT1 parkinsonism was similarly evaluated and marked reductions in striatal dopamine, 3,4-dihydroxyphenylacetic acid, and homovanillic acid content as well as the density of binding of all four dopaminergic ligands were measured.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Autoradiography
  • Carrier Proteins / analysis
  • Carrier Proteins / metabolism*
  • Corpus Striatum / chemistry
  • Corpus Striatum / metabolism
  • Corpus Striatum / pathology
  • Dopamine / analysis
  • Dopamine / metabolism*
  • Dopamine Plasma Membrane Transport Proteins
  • Dystonia Musculorum Deformans / metabolism*
  • Dystonia Musculorum Deformans / pathology
  • Humans
  • Membrane Glycoproteins / analysis
  • Membrane Glycoproteins / metabolism
  • Membrane Transport Proteins / analysis
  • Membrane Transport Proteins / metabolism
  • Middle Aged
  • Molecular Chaperones*
  • Nerve Tissue Proteins*
  • Neuropeptides*
  • Receptors, Dopamine / analysis
  • Receptors, Dopamine / metabolism
  • Vesicular Biogenic Amine Transport Proteins
  • Vesicular Monoamine Transport Proteins

Substances

  • Carrier Proteins
  • Dopamine Plasma Membrane Transport Proteins
  • Membrane Glycoproteins
  • Membrane Transport Proteins
  • Molecular Chaperones
  • Nerve Tissue Proteins
  • Neuropeptides
  • Receptors, Dopamine
  • TOR1A protein, human
  • Vesicular Biogenic Amine Transport Proteins
  • Vesicular Monoamine Transport Proteins
  • Dopamine