A 35-year-old woman presented with symptoms consistent with pheochromocytoma. Biochemical evaluation was equivocal. An MRI scan demonstrated an extra-adrenal high-intensity lesion on a T2-weighted sequence, which supported the suspicion of an extra-adrenal pheochromocytoma. Laparoscopically discovered to be located in the root of the small bowel mesentery, the 5-cm mass was excised along with a segment of small bowel. Pathology examination demonstrated fibromatosis, a benign lesion.