[Kasabach-Merritt syndrome in giant hemangioma of the liver. A case report]

Chirurg. 2002 Jul;73(7):729-32. doi: 10.1007/s00104-002-0445-1.
[Article in German]

Abstract

Kasabach-Merritt-syndrome is rare coagulation disorder with consumption coagulopathy caused by vascular malformations. We report the case of a 44-year-old woman with repeated severe bleeding complications after small and medium sized operations with normal results in the tests of plasmatic coagulation. After discovery of a giant hemangioma of the liver the diagnosis was established. Activation of coagulation was stopped preoperatively by i.v.-heparinization and curative treatment by right-sided hemihepatectomy followed.

Publication types

  • Case Reports
  • English Abstract

MeSH terms

  • Adult
  • Angiography, Digital Subtraction
  • Blood Coagulation Tests
  • Disseminated Intravascular Coagulation / etiology*
  • Disseminated Intravascular Coagulation / pathology
  • Disseminated Intravascular Coagulation / prevention & control
  • Female
  • Follow-Up Studies
  • Hemangioma / complications*
  • Hemangioma / diagnosis
  • Hemangioma / pathology
  • Hemangioma / surgery
  • Heparin / administration & dosage
  • Hepatectomy
  • Humans
  • Liver / pathology
  • Liver Neoplasms / complications*
  • Liver Neoplasms / diagnosis
  • Liver Neoplasms / pathology
  • Liver Neoplasms / surgery
  • Postoperative Hemorrhage / etiology*
  • Postoperative Hemorrhage / pathology
  • Postoperative Hemorrhage / prevention & control
  • Premedication
  • Reoperation
  • Syndrome
  • Thrombocytopenia / etiology*
  • Thrombocytopenia / pathology
  • Thrombocytopenia / prevention & control
  • Tomography, X-Ray Computed

Substances

  • Heparin