SIRT3, a human SIR2 homologue, is an NAD-dependent deacetylase localized to mitochondria

Proc Natl Acad Sci U S A. 2002 Oct 15;99(21):13653-8. doi: 10.1073/pnas.222538099. Epub 2002 Oct 8.

Abstract

The SIR2 (silent information regulator 2) gene family has diverse functions in yeast including gene silencing, DNA repair, cell-cycle progression, and chromosome fidelity in meiosis and aging. Human homologues, termed sirtuins, are highly conserved but are of unknown function. We previously identified a large imprinted gene domain on 11p15.5 and investigated the 11p15.5 sirtuin SIRT3. Although this gene was not imprinted, we found that it is localized to mitochondria, with a mitochondrial targeting signal within a unique N-terminal peptide sequence. The encoded protein was found also to possess NAD(+)-dependent histone deacetylase activity. These results suggest a previously unrecognized organelle for sirtuin function and that the role of SIRT3 in mitochondria involves protein deacetylation.

Publication types

  • Research Support, U.S. Gov't, Non-P.H.S.
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Amino Acid Sequence
  • Animals
  • Base Sequence
  • COS Cells
  • Chromosome Mapping
  • Chromosomes, Human, Pair 11 / genetics
  • Cloning, Molecular
  • Computational Biology
  • DNA, Complementary / genetics
  • Gene Expression
  • Histone Deacetylases / genetics*
  • Histone Deacetylases / isolation & purification
  • Histone Deacetylases / metabolism*
  • Humans
  • Mitochondria / enzymology
  • Mitochondrial Proteins / genetics*
  • Mitochondrial Proteins / isolation & purification
  • Mitochondrial Proteins / metabolism*
  • Molecular Sequence Data
  • Recombinant Fusion Proteins / genetics
  • Recombinant Fusion Proteins / metabolism
  • Sequence Homology, Amino Acid
  • Sirtuin 3
  • Sirtuins
  • Tissue Distribution

Substances

  • DNA, Complementary
  • Mitochondrial Proteins
  • Recombinant Fusion Proteins
  • SIRT3 protein, human
  • Sirtuin 3
  • Sirtuins
  • Histone Deacetylases