To categorize variant persistent müllerian-duct derivatives (MDD) in males and determine their related clinical presentations for further management, five male patients with retained MDDs from abnormal müllerian remnants were studied. They comprised one patient with persistent müllerian-duct syndrome, one with transverse testicular ectopia, two with mixed gonadal dysgenesis, and one with a müllerian-duct cyst. Removal of persistent müllerian-duct structures and genitoplasty were done in selected patients. Categorization of patients with persistent MDDs permits further understanding of the pathogenesis and facilitates the choice of treatment.