Renal cell carcinoma with t(X;17): singular pediatric neoplasm with specific phenotype/genotype features

Pediatr Dev Pathol. 2003 Jan-Feb;6(1):84-7. doi: 10.1007/s10024-002-1010-0. Epub 2002 Dec 10.

Abstract

Renal cell carcinomas in children are extremely rare and are usually associated with specific chromosomal rearrangements, different from those seen in adult patients. We present the case of a 9-year-old girl with a renal cell carcinoma with t(X;17) diagnosed at our institution. We also review the pertinent literature, with an emphasis on the genetic and molecular aspects associated with this rare neoplasm.

Publication types

  • Case Reports

MeSH terms

  • Biomarkers, Tumor / analysis
  • Carcinoma, Renal Cell / chemistry
  • Carcinoma, Renal Cell / genetics*
  • Carcinoma, Renal Cell / pathology
  • Carcinoma, Renal Cell / surgery
  • Child
  • Chromosome Aberrations
  • Chromosome Banding
  • Chromosomes, Human, Pair 17 / genetics*
  • Chromosomes, Human, X / genetics*
  • Female
  • Genotype
  • Humans
  • Immunohistochemistry
  • Karyotyping
  • Kidney Neoplasms / chemistry
  • Kidney Neoplasms / genetics*
  • Kidney Neoplasms / pathology
  • Kidney Neoplasms / surgery
  • Phenotype
  • Translocation, Genetic*
  • Treatment Outcome

Substances

  • Biomarkers, Tumor