Primary ciliary dyskinesia (PCD) is a rare genetic disease, in which a number of human organs are involved: upper and lower respiratory tract, spermatozoa in males and fallopian tube in females. In minority of cases PCD presents as Kartagener's syndrome (KS): sinusitis, bronchiectasis and inversion of internal organs. We report a case of Kartagener's syndrome in 43-year-old fertile male. After clinical and radiological examination and biopsy of the bronchial mucosa diagnosis of KS was established. The problem of fertility in KS males is discussed.