Merlin suppresses the SRE-dependent transcription by inhibiting the activation of Ras-ERK pathway

Biochem Biophys Res Commun. 2003 Mar 7;302(2):238-45. doi: 10.1016/s0006-291x(03)00124-4.

Abstract

The neurofibromatosis type 2 (NF2) gene encodes an intracellular membrane-associated protein called merlin or schwannomin, which is known to be a tumor suppressor. Numerous studies have suggested that merlin is involved in the regulation of cell growth and proliferation. Previously, merlin/schwannomin was reported to block Ras-induced cell proliferation and anchorage-independent cell growth. Also, the N-terminus of merlin was found to suppress cell proliferation, although it appears to be less effective than full-length merlin. However, the inhibitory mechanism of merlin is unknown. In this report, merlin is shown to be effective at suppressing serum/Ras-induced and Elk-mediated SRE dependent transactivation, and serum-induced ERK phosphorylation in NIH3T3 cells. In addition, merlin inhibited serum-induced Elk phosphorylation, a downstream effector of ERKs. Also, the N-terminal deficient merlin mutant could not block serum-induced and Elk-mediated SRE dependent transactivation, although the C-terminal deficient merlin mutant could. These results suggest that merlin inhibits SRE dependent transactivation by repressing serum-induced ERK phosphorylation and its downstream effector, Elk phosphorylation. Also, the N-terminus of merlin may be important for its inhibitory effect. Our results show that merlin acts as a negative regulator of the SRE signaling pathway via the Ras-ERKs pathway.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • 3T3 Cells
  • Animals
  • Enzyme Activation
  • Mice
  • Mitogen-Activated Protein Kinases / antagonists & inhibitors*
  • Mitogen-Activated Protein Kinases / metabolism
  • Neurofibromin 2 / chemistry
  • Neurofibromin 2 / pharmacology*
  • Phosphorylation
  • Protein Structure, Tertiary
  • Receptor, EphB1 / metabolism
  • Receptor, EphB1 / physiology
  • Serum Response Element / physiology*
  • Transcription, Genetic / drug effects*
  • ras Proteins / antagonists & inhibitors*
  • ras Proteins / metabolism

Substances

  • Neurofibromin 2
  • Receptor, EphB1
  • Mitogen-Activated Protein Kinases
  • ras Proteins