Management of haemophilia B inhibitor patients with anaphylactic reactions to FIX concentrates

Haemophilia. 2003 May;9(3):269-71. doi: 10.1046/j.1365-2516.2003.00772.x.

Abstract

Allergic reactions to concentrates containing factor IX (FIX) are serious complications in the treatment of haemophilia B patients with inhibitor. We have established a therapeutic protocol for such cases using an initial skin test followed by step-wise infusions of FIX concentrates under hydrocortisone cover. We have successfully treated three patients whose treatment with FIX had been suspended.

MeSH terms

  • Anaphylaxis / chemically induced*
  • Anti-Inflammatory Agents / therapeutic use
  • Child
  • Clinical Protocols
  • Drug Administration Schedule
  • Drug Eruptions / etiology
  • Factor IX / adverse effects*
  • Factor IX / antagonists & inhibitors
  • Factor IX / therapeutic use
  • Hemophilia B / drug therapy*
  • Humans
  • Hydrocortisone / therapeutic use
  • Skin Tests

Substances

  • Anti-Inflammatory Agents
  • Factor IX
  • Hydrocortisone