[Pourfour du Petit syndrome: a rare aetiology of unilateral exophtalmos with mydriasis and lid retraction]

Rev Med Interne. 2003 Apr;24(4):261-5. doi: 10.1016/s0248-8663(03)00029-8.
[Article in French]

Abstract

Introduction: Pourfour du Petit syndrome, rarely reported, is the opposite of Claude Bernard-Horner syndrome.

Exegeses: A 67 years old female is hospitalised for dysphagia, allowing the discovery of oesophagus carcinoma with mediastinal, pleural and costal extension. The discovery of left unilateral mydriasis associated with exophthalmos and eyelid retraction suggest Pourfour du Petit syndrome; this diagnosis is confirmed by CT-scan, finding pedicular lysis of high dorsal vertebras and intra-canalar tumoral extension.

Conclusion: Pourfour du Petit syndrome has the same localisation value and the same aetiologies as Claude Bernard-Horner syndrome, but its mechanism proceeds byan exciting lesion of cervical sympathetic nervous system. The recognition of this entity can allow the diagnosis of pathologies that need emergency treatment.

Publication types

  • Case Reports
  • English Abstract

MeSH terms

  • Aged
  • Autonomic Nervous System Diseases / etiology*
  • Deglutition Disorders / etiology
  • Esophageal Neoplasms / complications*
  • Esophageal Neoplasms / drug therapy
  • Exophthalmos / etiology*
  • Eyelid Diseases / etiology*
  • Fatal Outcome
  • Female
  • Humans
  • Mydriasis / etiology*
  • Rare Diseases / etiology*
  • Syndrome
  • Tomography, X-Ray Computed