Although dissecting aneurysms appear not to be as rare as previously reported, their etiology remains unclear. We describe a rare case of a girl with ischemia in the region of the posterior cerebral artery (PCA). The patient complained of a mild headache and left upper paresthesia. Neurological findings revealed a mild left hemiparesis. Visual field was intact, and cardiac embolism was excluded due to the almost normal chest X-p, ECG, and UCG. Laboratory findings were within normal limits. However, MRA and angiography revealed a linear shadow and an irregular caliber change at the right P1-P2 segment. Conservative therapy was pursued and the patient showed full neurological recovery. After a 3-month follow-up period, MRI showed no recurrence and MRA showed that the lesion had returned to normal. Here, we report the case as well as review the literature relating to this disorder, including discussion of its etiology, clinical features, radiological findings, and management strategies. We conclude that this disorder should be taken into consideration as a differential diagnosis of cerebrovascular disease in young people.