Orbital solitary fibrous tumor: report of two cases and literature review

Jpn J Ophthalmol. 2003 Jul-Aug;47(4):415-8. doi: 10.1016/s0021-5155(03)00071-6.

Abstract

Background: Solitary fibrous tumor (SFT) is a rare, benign, and very uncommon lesion in the orbit. Because of its complex and variable clinical and histological appearance the SFT is often misdiagnosed.

Cases: Two new cases of orbital SFT are reported, one in a man and the other in a woman, both unilateral and in the superomedial orbit.

Observations: Clinical and tomographical evaluations were conducted and the lesions were excised. The histological evaluation showed the tumors were composed of spindle-shaped cells within collagen bundles and vascular channels. Immunohistochemical staining was positive for CD 34 and negative for S-100 protein.

Conclusion: Immunohistochemical study is an important adjuvant in determining the SFT diagnosis. Long-term follow-up is necessary because of the possibility of SFT recurrence after excision.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Antigens, CD34 / analysis
  • Biomarkers, Tumor / analysis
  • Female
  • Fibroma / diagnostic imaging
  • Fibroma / pathology*
  • Fibroma / surgery
  • Humans
  • Male
  • Middle Aged
  • Orbital Neoplasms / diagnostic imaging
  • Orbital Neoplasms / pathology*
  • Orbital Neoplasms / surgery
  • S100 Proteins / analysis
  • Tomography, X-Ray Computed

Substances

  • Antigens, CD34
  • Biomarkers, Tumor
  • S100 Proteins