Detection of full fragile X mutation

Lancet. 1992 Feb 1;339(8788):271-2. doi: 10.1016/0140-6736(92)91334-5.

Abstract

In fragile X syndrome, the most common inherited cause of mental deficiency, the underlying mutation is a large increase in the number of CGG repeats in a gene on chromosome X. We have developed a polymerase chain reaction (PCR) method to amplify across the full mutation in affected individuals. In this report, a fragile X family including a positive prenatally diagnosed fetus was analysed by PCR, and the results are consistent with direct genomic Southern blot analysis. Genetic screening of at-risk populations for fragile X can now be achieved by PCR rapidly, inexpensively, and on small samples.

MeSH terms

  • Amino Acid Sequence
  • DNA / analysis*
  • Female
  • Fragile X Syndrome / genetics*
  • Genetic Carrier Screening / methods
  • Humans
  • Male
  • Molecular Sequence Data
  • Mutation / genetics*
  • Pedigree
  • Polymerase Chain Reaction / methods
  • Pregnancy
  • Prenatal Diagnosis / methods

Substances

  • DNA