IGF binding protein 3 in patients with Laron type dwarfism: effect of exogenous rIGF-I

Clin Endocrinol (Oxf). 1992 Mar;36(3):301-4. doi: 10.1111/j.1365-2265.1992.tb01449.x.

Abstract

Objective: The aim of the study was to investigate the serum levels of IGFBP-3, the major IGF-I binding protein, in patients with Laron type dwarfism (LTD) before and after IGF-I treatment.

Design and patients: Eight Laron type dwarfism patients (four children and four adults) were treated for 7 days by one daily s.c. injection of biosynthetic IGF-I in doses of 120 or 150 micrograms/kg/day.

Measurements: Blood was sampled in the fasting state before and 1 and 7 days after the last injection.

Results: It was found that IGF-I administration significantly reduced plasma hGH levels with recovery after one week of no treatment. Serum IGFBP-3 was abnormally low (0.70 +/- 0.37 mg/l) and decreased significantly further during IGF-I treatment (to 0.48 +/- 0.28 mg/l) (P less than 0.065).

Conclusions: The finding that serum IGFBP-3 is low in Laron type dwarfism, a disease due to molecular defects in the GH receptor, is compatible with the hypothesis that this IGF binding protein is GH-dependent. On the other hand the decrease during IGF-I administration and concomitant suppression of GH secretion may denote either that GH activity is not completely blocked in this syndrome or that there are additional mechanisms regulating IGFBP-3 synthesis.

MeSH terms

  • Adolescent
  • Adult
  • Carrier Proteins / blood*
  • Child
  • Child, Preschool
  • Dwarfism / blood*
  • Dwarfism / drug therapy
  • Female
  • Growth Hormone / blood
  • Humans
  • Insulin-Like Growth Factor Binding Proteins
  • Insulin-Like Growth Factor I / analysis
  • Insulin-Like Growth Factor I / therapeutic use*
  • Male
  • Recombinant Proteins / therapeutic use
  • Somatomedins / analysis*

Substances

  • Carrier Proteins
  • Insulin-Like Growth Factor Binding Proteins
  • Recombinant Proteins
  • Somatomedins
  • Insulin-Like Growth Factor I
  • Growth Hormone