Vulvar cicatricial pemphigoid of childhood

Pediatr Dermatol. 2004 Jan-Feb;21(1):51-3. doi: 10.1111/j.0736-8046.2004.21110.x.

Abstract

We report a 9-year-old girl with a vulvar autoimmune bullous dermatosis. A diagnosis of localized bullous pemphigoid or cicatricial pemphigoid was made on the basis of immunohistologic data. Since the lesions were unresponsive to topical corticosteroids but healed completely on dapsone at a dosage of 1.5 mg/kg/day, we favor the diagnosis of vulvar cicatricial pemphigoid. Only two such cases have been reported thus far. The diagnostic criteria and therapeutic modalities are discussed.

Publication types

  • Case Reports

MeSH terms

  • Child
  • Dapsone / administration & dosage*
  • Female
  • Humans
  • Pemphigoid, Benign Mucous Membrane / drug therapy*
  • Vulvar Diseases / drug therapy*

Substances

  • Dapsone