Extremely poor prognosis of pediatric acute lymphoblastic leukemia with translocation (9;22): updated experience

Leuk Lymphoma. 1992 Sep;8(1-2):75-9. doi: 10.3109/10428199209049820.

Abstract

Approximately five percent of pediatric acute lymphoblastic leukemias (ALL) contain a translocation (9;22)(q34;q11) which results in rearrangement of the bcr and abl genes. At a median follow-up of 5 years, we assessed the prognostic implications of translocation (9;22) in 434 children receiving intensive treatment for ALL. Four-year event-free and overall survivals were only 0% and 20%, respectively, in 15 children with translocation (9;22), but were 81% and 89%, respectively, in 419 children lacking translocation (9;22) (P < 0.001). Based on these findings, we recommend very intensive treatment approaches for all children with translocation (9;22)-positive ALL.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Adolescent
  • Bone Marrow Transplantation
  • Child
  • Child, Preschool
  • Chromosomes, Human, Pair 22*
  • Chromosomes, Human, Pair 9*
  • Female
  • Humans
  • Infant
  • Male
  • Precursor Cell Lymphoblastic Leukemia-Lymphoma / genetics*
  • Precursor Cell Lymphoblastic Leukemia-Lymphoma / mortality*
  • Precursor Cell Lymphoblastic Leukemia-Lymphoma / surgery
  • Prognosis
  • Survival Rate
  • Translocation, Genetic*