Hyperandrogenism in a postmenopausal woman presenting with a metastatic ileum endocrine tumor

Fertil Steril. 2004 Mar;81(3):675-8. doi: 10.1016/j.fertnstert.2003.07.040.

Abstract

Objective: To elucidate the mechanism of the hyperandrogenism found in a postmenopausal woman presenting an ileum endocrine tumor with ovarian metastases.

Design: Case report.

Setting: University hospital.

Patient(s): A postmenopausal woman was referred for hirsutism. Basal plasma testosterone was high, 6.6 nM/L (normal, <or=0.7 nM/L). Pelvic magnetic resonance imaging revealed a 6-cm left ovarian mass.

Intervention(s): Bilateral salpingo-oophorectomy was performed. Pathological examination found a bilateral metastatic endocrine ovarian tumor, associated with a functional stroma. A primary ileum endocrine tumor was discovered and resected.

Main outcome measure(s): Immunohistochemical study of the expression of steroidogenic enzymes and beta and alpha subunits of hCG.

Result(s): Immunohistochemical expression of steroidogenic enzymes was found in the ovarian stromal tissue surrounding the tumor but not in the metastatic tumoral cells. A substantial percentage of the metastatic tumoral cells was immunopositive for the beta and alpha subunit of hCG but not the ileal cells.

Conclusion(s): These data suggest an hCG paracrine effect of the ovarian metastases tumor on the adjacent interstitial cells, resulting in the virilization of the patient.

Publication types

  • Case Reports

MeSH terms

  • Cholesterol Side-Chain Cleavage Enzyme / metabolism
  • Chorionic Gonadotropin, beta Subunit, Human / metabolism
  • Endocrine Gland Neoplasms / complications*
  • Endocrine Gland Neoplasms / metabolism
  • Endocrine Gland Neoplasms / pathology
  • Endocrine Gland Neoplasms / secondary
  • Female
  • Hirsutism / etiology*
  • Humans
  • Hyperandrogenism / etiology*
  • Ileal Neoplasms / complications*
  • Ileal Neoplasms / metabolism
  • Ileal Neoplasms / pathology
  • Ileal Neoplasms / secondary
  • Immunohistochemistry
  • Middle Aged
  • Ovarian Neoplasms / pathology
  • Postmenopause*
  • Steroid 17-alpha-Hydroxylase / metabolism

Substances

  • Chorionic Gonadotropin, beta Subunit, Human
  • Steroid 17-alpha-Hydroxylase
  • Cholesterol Side-Chain Cleavage Enzyme