Mental retardation, Robin sequence, and brachydactyly: further confirmation of a new syndrome

Am J Med Genet A. 2004 Apr 15;126A(2):204-7. doi: 10.1002/ajmg.a.20575.

Abstract

Recently we reported two sibs, brother and sister, with a new multiple congenital anomalies/mental retardation (MCA/MR) syndrome characterized by mild to moderate psychomotor delay, Robin sequence, distinctive facial appearance, and brachydactyly. We have subsequently observed a similar pattern of anomalies in two unrelated patients who also showed additional clinical findings. This new observation supports the existence of a new syndrome and expands the phenotypic spectrum of the condition.

Publication types

  • Case Reports

MeSH terms

  • Abnormalities, Multiple / genetics
  • Abnormalities, Multiple / pathology
  • Child, Preschool
  • Female
  • Genes, Recessive
  • Hand Deformities, Congenital / diagnostic imaging
  • Hand Deformities, Congenital / genetics
  • Hand Deformities, Congenital / pathology*
  • Humans
  • Intellectual Disability / genetics
  • Intellectual Disability / pathology*
  • Male
  • Pierre Robin Syndrome / genetics
  • Pierre Robin Syndrome / pathology*
  • Radiography