Plasma D-penicillamine redox state evaluation by capillary electrophoresis with laser-induced fluorescence

J Chromatogr B Analyt Technol Biomed Life Sci. 2004 Apr 25;803(2):299-304. doi: 10.1016/j.jchromb.2004.01.002.

Abstract

D-Penicillamine (D-Pen) is a thiol drug used in the treatment of Wilson's disease, rheumatoid arthritis, metal intoxication and cystinuria. We have recently described a new capillary electrophoresis (CE) method to measure physiological thiols, in which separation of total plasma homocysteine, cysteine, cysteinylglycine, glutathione is achieved using the organic base N-methyl-D-glucamine in the run buffer. In this paper, we present an improvement of our method that allows a baseline separation of total plasma D-Pen from the physiological thiols. Moreover, reduced, free and protein-bound forms of drug are measured by varying the order of disulfide reduction with tributylphosphine and proteins precipitation with 5-sulphosalicylic acid (SSA). After derivatization with 5-iodoacetamidofluorescein (5-IAF), samples are separated and measured by capillary electrophoresis with laser-induced fluorescence in an uncoated fused-silica capillary (57 x 75 microm i.d.) using a phosphate/borate run buffer pH 11.4. In these conditions, the migration time of D-Pen is about 7 min and the time required for each analysis is roughly 10 min. The proposed method has been utilized to measure the various forms of the drug in a D-Pen administered Wilson's disease patient.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Fluorescence
  • Hepatolenticular Degeneration / blood
  • Hepatolenticular Degeneration / drug therapy
  • Humans
  • Lasers
  • Oxidation-Reduction
  • Penicillamine / blood*
  • Penicillamine / therapeutic use
  • Reproducibility of Results
  • Sensitivity and Specificity

Substances

  • Penicillamine