Syncytial giant-cell hepatitis--a specific disease entity?

J Hepatol. 1992 May;15(1-2):216-9. doi: 10.1016/0168-8278(92)90039-r.

Abstract

Syncytial giant-cell hepatitis was recently reported to be related to a paramyxovirus and carried a poor prognosis. Twelve patients with syncytial giant-cell hepatitis seen in an 8 1/2-year period in our institute were reviewed. Seven patients had an identifiable aetiological cause: two had autoimmune chronic active hepatitis, one had primary sclerosing cholangitis and autoimmune chronic active hepatitis, two presented with prolonged jaundice after acute hepatitis A and B, one had chronic Epstein-Barr virus infection and the remaining patient was seropositive for antibody to hepatitis C virus. One patient with autoimmune chronic active hepatitis who had frequent syncytial giant cells in the liver responded promptly to corticosteroid treatment and a repeated biopsy 3 years later showed histological improvement with a marked decrease in the number of syncytial giant cells. Of the remaining five patients, three ran a clinical course of fulminant hepatic failure and two had severe chronic active hepatitis. These data indicate that syncytial giant-cell hepatitis is unlikely to be related to only one single aetiological agent and that syncytial giant-cell hepatitis does not always carry an ominous prognosis.

MeSH terms

  • Adolescent
  • Adrenal Cortex Hormones / therapeutic use
  • Adult
  • Aged
  • Biopsy
  • Child
  • Female
  • Giant Cells / ultrastructure*
  • Hepatitis Antibodies / analysis
  • Hepatitis, Viral, Human / etiology*
  • Hepatitis, Viral, Human / pathology
  • Humans
  • Male
  • Middle Aged
  • Paramyxoviridae / isolation & purification
  • Prognosis
  • Radioimmunoassay
  • Terminology as Topic
  • Time Factors

Substances

  • Adrenal Cortex Hormones
  • Hepatitis Antibodies