Aortopulmonary septal defect, interrupted aortic arch, aortic origin of the right pulmonary artery, intact ventricular septum, and patent ductus arteriosus (Berry Syndrome) is a rarely reported malformation. A 6-day-old girl underwent successful one-stage complete repair of direct anastomosis between the ascending and descending aorta, reimplantation of the right pulmonary artery augmented with pericardium patch. Stenosis of the origin of the reimplanted right pulmonary artery was treated by balloon angioplasty at the age of 3 months. The authors emphasize the additive nature of surgical correction and interventional cardiology. Review of the literature reveals this patient to be the 25th reported case with Berry syndrome, and the first of that in Hungary.